New International League Against Epilepsy Epilepsy Syndrome Classification: Classification and Definition of Epilepsy Syndromes with Onset at a Variable Age

Although epilepsy syndromes have been recognized for over 50 years, no formally accepted International League Against Epilepsy (ILAE) classification of has existed until recently. The ILAE Task Force on Nosology and Definitions Taskforce (2017–2021) defined an syndrome as “a characteristic cluster clinical electroencephalographic features, often supported by specific etiological findings (structural, genetic, metabolic, immune, infectious).” Syndromes can be divided into generalized, focal, combined generalized focal syndromes. Some associated with developmental and/or epileptic encephalopathy or progressive neurological deterioration. Two etiology-specific seizure onset at a variable age. diagnosis is clinically important because it frequently carries prognostic treatment implications. goal this review to provide updated diagnostic criteria the that age onset, based special report published in 2022. Key words: Classification; Terminology; syndrome; Progressive myoclonic epilepsies.